ICVTS Click here for other ICVTS advertising opportunities
HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS
QUICK SEARCH:   [advanced]


     

Interact CardioVasc Thorac Surg 2008;7:222-226. doi:10.1510/icvts.2007.171611
© 2008 European Association of Cardio-Thoracic Surgery
This Article
Right arrow Full Text
Right arrow Full Text (PDF)
Right arrow Alert me when this article is cited
Right arrow Alert me if a correction is posted
Services
Right arrow Email this article to a friend
Right arrow Similar articles in this journal
Right arrow Similar articles in PubMed
Right arrow Alert me to new issues of the journal
Right arrow Add to Personal Folders
Right arrow Download to citation manager
Right arrow Author home page(s):
Sandro Gelsomino
Roberto Lorusso
Pierluigi Stefàno
Right arrow Permission Requests
Citing Articles
Right arrow Citing Articles via Google Scholar
Google Scholar
Right arrow Articles by Gelsomino, S.
Right arrow Articles by Gensini, G. F.
Right arrow Search for Related Content
PubMed
Right arrow PubMed Citation
Right arrow Articles by Gelsomino, S.
Right arrow Articles by Gensini, G. F.
Related Collections
Right arrow Anesthesia
Right arrow Valve disease

Institutional report - Cardiac general

Cardiac surgery in type-1-myotonic muscular dystrophy (Steinert syndrome) associated to Barlow disease

Sandro Gelsominoa,*, Roberto Lorussob, Giuseppe Billèa, Giuseppe De Ciccob, Ugo Da Broic, Carlo Rostagnoa, Pierluigi Stefànoa and Gian Franco Gensinia

a Experimental Surgery Unit, Cardiac Surgery, Department of Heart and Vessels, Careggi Hospital, Viale Morgagni 85, 50134, Florence, Italy
b Cardiac Surgery, Civic Hospital, Brescia, Italy
c Anesthesia, Santa Maria della Misericordia Hospital, Udine, Italy

*Corresponding author. Tel.: +39-055-794-7467; fax: +39-055-794-7628.

E-mail address: sandro.gelsomino{at}libero.it (S. Gelsomino).

No data exist in the English-language literature about patients with Barlow disease associated to Steinert syndrome and little is known about the employment of hypothermic cardiopulmonary bypass (CPB) and hyperkalemic cardioplegia in these patients. We present our experience with six patients affected by myxomatous degeneration associated to Steinert disease undergoing complex mitral valve repair. In all patients we employed mild hypothermic CPB (31 °C) and myocardial protection was achieved, in the entire cohort, by the use of blood hyperkalemic cold cardioplegia. The postoperative course was uneventful in all patients and neither shivering nor generalized muscle contraction were observed. Furthermore, all patients have remained well on an outpatient basis. Hypothermic CPB and hyperkalemic cardioplegia can be safely employed in patients with Steinert syndrome requiring complex cardiac surgery. Further large studies are necessary to confirm our findings.

Key Words: Myotonic muscular dystrophy; Steinert disease; Mitral repair; Barlow disease

HOME HELP FEEDBACK SUBSCRIPTIONS ARCHIVE SEARCH TABLE OF CONTENTS
ANN THORAC SURG ASIAN CARDIOVASC THORAC ANN EUR J CARDIOTHORAC SURG
J THORAC CARDIOVASC SURG ICVTS ALL CTSNet JOURNALS
Copyright © 2008 European Association for Cardio-thoracic Surgery